PIG-A noob muaj nyob ntawm X chromosome. Txawm hais tias tsis yog ib qho kab mob los ntawm kev xeeb tub, PNH yog kab mob caj ces, lub npe hu ua kev mob caj ces. Cov kab mob qog ntshav uas cuam tshuam dhau qhov hloov pauv PIG-A rau tag nrho nws cov xeeb leej xeeb ntxwv-liab hlwb, leukocytes (xws li lymphocytes), thiab platelets.
YPuas yog paroxysmal nocturnal hemoglobinuria keeb kwm?
Tus mob no tau txais, dua li qub. Nws tshwm sim los ntawm kev hloov pauv tshiab hauv PIGA noob, thiab feem ntau tshwm sim hauv cov neeg uas tsis muaj keeb kwm yav dhau los ntawm kev tsis sib haum xeeb hauv lawv tsev neeg. Tus mob no tsis dhau mus rau cov menyuam yaus ntawm cov tib neeg cuam tshuam.
Puas yog paroxysmal txias hemoglobinuria caj ces?
(Yog xav paub ntxiv txog qhov teeb meem no, xaiv "paroxysmal nocturnal hemoglobinuria" raws li koj cov lus tshawb fawb hauv Cov Ntaub Ntawv Tsis Muaj Kab Mob.) Tau txais hemolytic anemias yog tsis yog caj ces hauv keeb kwm.
Dab tsi ua rau paroxysmal nocturnal hemoglobinuria?
PNH tshwm sim thaum kev hloov pauv ntawm PIG-A noob tshwm sim hauv cov pob txha pob txha stem cell Cov qia hlwb ua rau tag nrho cov ntshav loj hlob suav nrog cov qe ntshav liab (RBC), uas nqa oxygen rau peb cov ntaub so ntswg; Cov qe ntshav dawb (WBC), uas tiv thaiv kab mob; thiab platelets (PLT), uas koom nrog hauv kev tsim cov ntshav txhaws.
YPuas yog paroxysmal nocturnal hemoglobinuria autoimmune?
Paroxysmal txias hemoglobinuria yog ib qho tsis tshua muaj autoimmune hemolytic teeb meem tus yam ntxwv los ntawm kev puas tsuaj ntxov ntxov ntawm cov qe ntshav liab noj qab haus huv (hemolysis) feeb mus rau cov xuab moos tom qab kis tau khaub thuas.
