Methemoglobinemia, lossis methaemoglobinemia, yog ib yam mob ntawm methemoglobin siab hauv cov ntshav. Cov tsos mob yuav muaj xws li mob taub hau, kiv taub hau, ua tsis taus pa luv, xeev siab, tsis zoo cov leeg nqaij, thiab daim tawv nqaij xiav (cyanosis). Cov teeb meem muaj xws li qaug dab pegthiab lub plawv arrhythmias.
methemoglobinemia cuam tshuam rau lub cev li cas?
Autosomal recessive congenital methemoglobinemia yog ib qho mob tshwm sim uas feem ntau cuam tshuam rau kev ua haujlwm ntawm cov qe ntshav liab. Tshwj xeeb, nws hloov cov molecule hauv cov hlwb hu ua hemoglobin. Hemoglobin nqa oxygen mus rau cov hlwb thiab cov ntaub so ntswg thoob plaws lub cev.
Puas yog methemoglobinemia ua rau tuag taus?
Methemoglobinemia yog ib qho txawv txav thiab muaj peev xwm ua rau tuag tausuas hemoglobin tau oxidized rau methemoglobin thiab poob nws lub peev xwm los khi thiab thauj oxygen.
Dab tsi yog qhov pheej hmoo ntawm methemoglobinemia?
Dab tsi ua rau tau txais methemoglobinemia thiab dab tsi yog qhov txaus ntshai?
- Fetal hemoglobin tuaj yeem oxidize yooj yim dua li cov neeg laus hemoglobin.
- Qib NADH reductase qis thaum yug los thiab nce nrog hnub nyoog; nws mus txog rau cov neeg laus thaum muaj hnub nyoog 4 hli.
Vim li cas methemoglobinemia ua rau cyanosis?
Methemoglobinemia yog ib yam mob uas tshwm sim los ntawm qhov ntau ntawm hemoglobin uas cov hlau ntawm heme yog oxidized rau ferric (Fe 3+ ) form. Methemoglobin tsis muaj txiaj ntsig li cov pa oxygen thiab yog li ua rau muaj kev sib txawv ntawm cyanosis.
