Cystinuria feem ntau tshwm sim los ntawm kev tsim cov amino acid, cystine, nyob rau hauv ob lub raum thiab zais zisQhov no ua rau tsim cov cystine muaju thiab / lossis pob zeb uas tuaj yeem thaiv cov pob zeb. tso zis. Cov tsos mob thiab cov tsos mob ntawm cystinuria yog qhov tshwm sim ntawm pob zeb tsim thiab tej zaum yuav muaj xws li: xeev siab.
cystinuria yog dab tsi?
Cystinuria yog ib qho kev cuam tshuam ntawm metabolic uas tshwm sim los ntawm ntau ntau ntawm cov cystine tsis tau nyob hauv cov zis, nrog rau peb cov tshuaj amino acids zoo sib xws: arginine, lysine, thiab ornithine.
Puas yog cystinuria yog kab mob raum?
Cystinuria yog ib yam kab mob uas ua rau pob zeb ua los ntawm cov amino acid cystine tsim nyob rau hauv ob lub raum, zais zis, thiab ureters. Cov kab mob sib kis tau dhau los ntawm niam txiv mus rau menyuam yaus los ntawm qhov tsis xws luag hauv lawv cov noob. Yuav kom tau cystinuria, ib tug neeg yuav tsum tau txais qhov tsis xws luag los ntawm ob niam txiv.
YPuas cystinuria zoo ib yam li cystinosis?
Cystinosis yog kab mob ntawm cystine cia nyob rau hauv uas lub raum yog thawj zaug, tab sis tsis yog tib lub hom phiaj. Cystinuria yog ib yam kab mob ntawm lub raum tubular cystine thauj nyob rau hauv uas ntau heev poob ntawm no insoluble amino acid ua rau nag lossis daus ntawm physiologic zis pH thiab concentration.
Kev kuaj mob cystinuria li cas?
Kev kuaj mob ntawm cystinuria yog npaj tau los ntawm kev tshuaj ntsuam pob zeb, kuaj xyuas cov zis, thiab kuaj zis 24-teev. Txawm hais tias kev phais mob yog qhov tsim nyog, lub hauv paus ntawm kev kho mob yog kev noj haus thiab kev kho mob tiv thaiv kev tsim pob zeb.
