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Puas yog keeb kwm hemochromatosis ua rau ntshav ntshav?

Cov txheej txheem:

Puas yog keeb kwm hemochromatosis ua rau ntshav ntshav?
Puas yog keeb kwm hemochromatosis ua rau ntshav ntshav?

Video: Puas yog keeb kwm hemochromatosis ua rau ntshav ntshav?

Video: Puas yog keeb kwm hemochromatosis ua rau ntshav ntshav?
Video: Thaksin Keeb Kwm Puas Yog Hmoob? 08/25/2019 2024, Tej zaum
Anonim

Hereditary hemochromatosis yog ib qho mob ntawm dysregulated hlau homeostasis uas ua rau cov hlau ntau dhau lawm. Hemochromatosis ua rau pulmonary, pancreatic, thiab hepatic dysfunction, tag nrho cov uas muaj feem cuam tshuam rau ntshav ntshav hauv cov pejxeem.

Koj puas tuaj yeem muaj hlau ntau thiab ntshav ntshav?

Hypochromic microcytic anemia nrog hlau ntau dhau tuaj yeem ua rau tawv nqaij daj ntseg (pallor), nkees (qaug zog), thiab kev loj hlob qeeb. Hauv hypochromic microcytic anemia nrog cov hlau ntau dhau, cov hlau uas tsis siv los ntawm cov qe ntshav liab sau nyob rau hauv daim siab, uas tuaj yeem cuam tshuam nws txoj haujlwm dhau sijhawm.

Koj ua li cas kho ntshav ntshav nrog hemochromatosis?

Cov neeg mob cuam tshuam nrog ntshav ntshav tsis tuaj yeem kho nrog phlebotomy. Yog li, daim ntawv thov ntawm cov neeg ua haujlwm hlau chelation(piv txwv li, deferoxamine, deferiprone, deferasirox) raug pom zoo. Deferoxamine tau muab tso rau hauv cov hlab ntsha lossis subcutaneously ntawm koob tshuaj txij li 25 txog 40 mg / kg.

Yuav ua li cas ntshav ntshav ua rau hemochromatosis?

Secondary hemochromatosis yog tshwm sim los ntawm cov hlau ntau dhau hauv kev noj zaub mov lossis los ntawm ntau qhov sib txuas ntawm cov ntshav. Qhov ib txwm ua rau cov hemochromatosis theem nrab yog cov ntshav muab rau cov hom ntshav qab zib hnyav, xws li kab mob qog nqaij hlav txuas lossis thalassemias txuas.

Koj puas muaj hlau deficiency anemia thiab hemochromatosis?

Nyob rau hauv cov neeg mob uas tsis muaj hlau tsis muaj ntshav liab, cov ntshav liab thiab cov ntshav hloov pauv yog qhov txawv txav qis; thiab nyob rau hauv cov neeg mob uas muaj keeb kwm hemochromatosis cov ntshav ntshav thiab cov ntshav hloov pauv tuaj yeem ua rau muaj qhov tsis zoo.

Pom zoo: