Cov txheej txheem:
- Puas yog methemoglobinemia yog qhov teeb meem tseem ceeb lossis rov ua haujlwm?
- Yuav ua li cas methemoglobinemia tuaj yeem tshwm sim?
- YYam hloov pauv yam twg yog methemoglobin?
- Ntau npaum li cas methemoglobin?
Video: Puas yog methemoglobin tseem ceeb lossis thim rov qab?
2024 Tus sau: Fiona Howard | [email protected]. Kawg hloov kho: 2024-01-10 06:38
Tus qauv qub txeeg qub teg ntawm daim ntawv enzyme deficiency hauv lub cev yog autosomal recessive Hb M yog los ntawm tus qauv autosomal dominant. Tsis muaj kev koom tes ntawm kev sib deev thiab qhov zaus ntawm congenital methemoglobinemia methemoglobinemia Methemoglobinemia tshwm sim thaum cov qe ntshav liab (RBCs) muaj methemoglobin nyob rau theem siab dua 1% Qhov no tuaj yeem yog los ntawm congenital ua, nce synthesis, los yog txo qhov kev tshem tawm. Kev nce qib kuj tseem tuaj yeem tshwm sim los ntawm kev cuam tshuam rau cov co toxins uas cuam tshuam rau cov tshuaj tiv thaiv redox, nce qib methemoglobin. https://emedicine.medscape.com › article › 204178-overview
Methemoglobinemia: Xyaum Qhov Tseem Ceeb, Keeb Kwm …
Puas yog methemoglobinemia yog qhov teeb meem tseem ceeb lossis rov ua haujlwm?
Congenital/Genetic/Hereditary Methemoglobinemia
Nws yog ib qho autosomal dominant mob Hauv cov tib neeg no, hemoglobin ruaj khov dua hauv nws daim ntawv oxidized thiab tiv taus kom txo tau. Muaj plaub hom NADH cytochrome b5 reductase deficiencies, tag nrho cov uas yog autosomal recessive disorders: 1.
Yuav ua li cas methemoglobinemia tuaj yeem tshwm sim?
Methemoglobinemia tuaj yeem yog vim qee yam tshuaj, tshuaj, lossis zaub mov lossis nws tuaj yeem tau txais los ntawm tus neeg niam txiv Cov tshuaj muaj xws li benzocaine, nitrates, lossis dapsone. Cov txheej txheem hauv qab no suav nrog qee cov hlau hauv hemoglobin hloov pauv los ntawm ferrous [Fe2+] rau ferric [Fe 3+] form.
YYam hloov pauv yam twg yog methemoglobin?
Hemoglobin uas muaj ferric hlau hu ua methemoglobin. HBB noob hloov uas ua rau methemoglobinemia, beta-globin hom hloov pauv cov qauv ntawm beta-globin thiab txhawb cov heme hlau hloov ntawm ferrous mus rau ferric. Cov hlau ferric tsis tuaj yeem khi cov pa oxygen thiab ua rau cyanosis thiab xim xim av.
Ntau npaum li cas methemoglobin?
Cov lus xaus thiab qhov cuam tshuam: Tag nrho qhov muaj feem ntau ntawm methemoglobinemia yog qis ntawm 0.035%; txawm li cas los xij, muaj kev pheej hmoo ntau ntxiv hauv cov neeg mob pw hauv tsev kho mob thiab nrog tshuaj loog benzocaine.
Pom zoo:
Puas yog alanine tseem ceeb lossis tsis tseem ceeb?
No tseem ceeb amino acids suav nrog: alanine, arginine, asparagine, aspartic acid, cysteine, glutamic acid, glutamine, glycine, proline, serine, thiab tyrosine. Cov tshuaj amino acids feem ntau tsis tseem ceeb, tshwj tsis yog thaum muaj mob thiab kev ntxhov siab .
Cov ntshav qab zib mellitus puas tuaj yeem thim rov qab?
Txawm hais tias tsis muaj kev kho mob ntshav qab zib hom 2, kev tshawb fawb qhia tias qee tus neeg tuaj yeem thim rov qab. Los ntawm kev hloov pauv kev noj haus thiab kev poob phaus, koj tuaj yeem ncav cuag thiab tuav cov ntshav qab zib ib txwm tsis muaj tshuaj.
Puas rov sau npe rov qab thim qhov txuas ntxiv?
Cov tswv cuab uas yav dhau los txuas ntxiv lawv lub sijhawm tso npe vim yog lub luag haujlwm kev pabcuam rau kev hloov pauv, kev cob qhia, lossis kev nce qib, tuaj yeem tshem tawm cov kev txuas ntxiv ua ntej lawv hnub ua haujlwm (thaum koj qhov txuas ntxiv pib pib) txhawm rau ua kom tau txais kev tso npe tam sim thiab muaj cai rau SRB .
Puas yog mob ntshav qab zib mellitus tuaj yeem thim rov qab?
MODY yog tshwm sim los ntawm kev hloov pauv caj ces dhau los ntawm tsev neeg. Tam sim no tsis muaj txoj hauv kev los tiv thaiv lossis kho nws, tab sis nws tuaj yeem tswj tau, thiab kwv yees . Puas metformin ua haujlwm rau MODY? Lus xaus:
Pob ntseg puas yuav thim rov qab tom qab ntsuas?
Yog koj ncab koj pob ntseg ib xyoos dhau los lossis ob peb lub hlis dhau los, koj pob ntseg muaj peev xwm thim rov qab mus rau nws qhov loj duayog tias nws tau ncab thiab kho tau ntau xyoo . pob ntseg rov zoo li qub tom qab ntsuas? Cov neeg feem coob tuaj yeem mus ntawm 2g (6mm) - 00g (10mm) thiab cia siab tias lawv lub pob ntseg rov qab mus rau qhov qub tho, tom qab ob peb lub hlis kho.