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Puas yog myeloproliferative disorders?

Cov txheej txheem:

Puas yog myeloproliferative disorders?
Puas yog myeloproliferative disorders?

Video: Puas yog myeloproliferative disorders?

Video: Puas yog myeloproliferative disorders?
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Cov ntaub ntawv tsev neeg ntawm myeloproliferative neoplasms (MPN) thiab kev pab cuam caj ces rau cov xwm txheej ntawm MPN tau ntev tau lees paub. Feem ntau ntawm cov xwm txheej, tsev neeg MPN tau txais txiaj ntsig raws li qhov tseem ceeb ntawm autosomal dominant trait Qhov kev nkag mus txawv ntawm ib ncig ntawm 20% mus txog rau 100% hauv qee cov pedigrees.

YPuas yog myeloproliferative neoplasm hereditary?

Rau ntau tsev neeg, MPN tau txais los ntawm tus qauv autosomal dominant[Kralovics li al. 2003b; Rumi et al. 2006], whereas rau lwm tsev neeg penetrance ntawm tus kab mob yog me ntsis txo, thiab ib co muaj ib tug recessive qauv [Rumi li al. 2007].

Koj tuaj yeem nyob nrog tus kab mob myeloproliferative ntev npaum li cas?

Cov neeg feem coob uas muaj qhov tseem ceeb thrombocythemia thiab polycythemia vera nyob ntau dua 10 mus rau 15 xyoo nrog qee qhov teeb meem. Cov neeg uas muaj myelofibrosis nyob kwv yees li tsib xyoos thiab qee zaum, tus kab mob tuaj yeem ua rau mob leukemia.

Puas yog myeloproliferative teeb meem yog hom mob qog noj ntshav?

Cov kab mob myeloproliferative mob ntev yog ib pawg ntawm mob qog nqaij hlav hauv ntshav qisuas cov pob txha pob txha ua rau ntau cov qe ntshav liab txawv txav, cov qe ntshav dawb, lossis cov platelets, uas nyob hauv cov pob txha. ntshav.

Dab tsi yog qhov mob myeloproliferative tshaj plaws?

Polycythemia Vera Nov yog qhov mob myeloproliferative tshaj plaws.

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