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Puas yog spongiform encephalopathy hereditary?

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Puas yog spongiform encephalopathy hereditary?
Puas yog spongiform encephalopathy hereditary?

Video: Puas yog spongiform encephalopathy hereditary?

Video: Puas yog spongiform encephalopathy hereditary?
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Feem ntau, tus neeg cuam tshuam tau txais cov noob hloov pauv los ntawm ib tus niam txiv cuam tshuamHauv qee tus neeg, tsev neeg cov kab mob prion yog tshwm sim los ntawm kev hloov pauv tshiab hauv PRNP noob. Txawm hais tias cov neeg zoo li no feem ntau tsis muaj leej niam leej txiv cuam tshuam, lawv tuaj yeem dhau qhov kev hloov caj ces rau lawv cov menyuam.

Puas spongiform encephalopathy tuaj yeem tau txais txiaj ntsig?

TSEs feem ntau yog qhov tsis sib xws thiab tshwm sim hauv cov tsiaj uas tsis muaj kev hloov pauv protein ntau. Inherited TSE tshwm sim nyob rau hauv cov tsiaj nqa ib tug tsawg mutant prion allele, uas qhia prion proteins uas contort los ntawm lawv tus kheej mus rau hauv tus kab mob-ua conformation.

Yuav ua li cas thiaj tau spongiform encephalopathy?

Kev tshawb fawb qhia tias vCJD tuaj yeem ua rau los ntawm tib neeg noj nqaij nyuj los ntawm nyuj nrog tus kab mob TSEhu ua bovine spongiform encephalopathy (BSE), tseem hu ua "tus kab mob nyuj vwm."Lwm TSEs pom nyob rau hauv cov tsiaj muaj xws li scrapie, uas cuam tshuam rau yaj thiab tshis; kab mob nkim ntev, uas cuam tshuam rau elk thiab mos lwj; thiab …

Is TSE genetic?

Cov kab mob caj ces TSE sawv cev 17.7% ntawm tag nrho cov kab mob TSE, suav nrog cov kab mob sib kis, iatrogenic, thiab variant CJD. Qhov kev hloov pauv ntau zaus yog V210I (n=54), thiab qhov thib ob feem ntau yog E200K (n=42).

Dab tsi yog qhov kis tau tus mob spongiform encephalopathy ntau tshaj plaws?

Creutzfeldt-Jakob tus kab mob lossis CJD yog ib qho kev puas siab puas ntsws uas kho tsis tau thiab ua rau tuag taus. Nws yog qhov feem ntau ntawm cov hom kis tau tus mob spongiform encephalopathy pom hauv tib neeg.

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